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絲氨酸羧甲半胱氨酸合成酶重組兔單抗

簡要描述:The protein encoded by this gene acts as a homotetramer to catalyze the conversion of homocysteine to cystathionine, the first step in the transsulfuration pathway. The encoded protein is allosterically activated by adenosyl-methionine and uses pyridoxal phosphate as a cofactor. Defects in this gene can cause cystathionine beta-synthase deficiency (CBSD), which can lead to homocystinuria. Multiple alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, May

  • 產(chǎn)品型號:bsm-61957R
  • 廠商性質(zhì):生產(chǎn)廠家
  • 更新時間:2025-03-01
  • 訪  問  量: 118

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Human
WB,IHC-P,IHC-F,ICC/IF,IF
Store at 4℃ for short term. Store at -20℃ for long term. Avoid repeated freeze/thaw cycles.

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